ICD-11 code : 8B60.6;
Preferred Label : Monomelic amyotrophy;
ICD-11 definition : Atrophy and weakness restricted to one upper or lower limb, onset in the second or
third decade, male predominance, and sporadic occurrence are characteristic features
of MMA. Other typical features include: insidious onset of lower motor neuron signs
due to anterior horn cell involvement, absence of upper motor neuron signs, slow progression
followed by stabilization within a few years,, and a benign symptomatic disease course.
MMA is particularly prevalent in Asia although is encountered worldwide.;
Origin ID : 2090347823;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
Atrophy and weakness restricted to one upper or lower limb, onset in the second or
third decade, male predominance, and sporadic occurrence are characteristic features
of MMA. Other typical features include: insidious onset of lower motor neuron signs
due to anterior horn cell involvement, absence of upper motor neuron signs, slow progression
followed by stabilization within a few years,, and a benign symptomatic disease course.
MMA is particularly prevalent in Asia although is encountered worldwide.