ICD-11 code : 1C1C.1;
Preferred Label : Waterhouse-Friderichsen syndrome;
ICD-11 definition : A syndrome of the adrenal glands, commonly caused by an infection with meningococcus
Neisseria meningitidis. This syndrome is characterized by bleeding into the adrenal
glands due to the severe bacterial infection. This syndrome may present with fever,
chills, vomiting, myalgia, or rash, with progression to disseminated intravascular
coagulation. Transmission is by direct contact or droplet transmission.;
ICD-11 synonym : Waterhouse-Friderichsen disease; meningococcal adrenal syndrome; acute adrenal insufficiency with meningococcal septicaemia; haemorrhagic meningococcal adrenitis; meningococcal Waterhouse-Friderichsen syndrome; Meningococcal haemorrhagic adrenalitis; adrenal haemorrhage syndrome;
ICD-11 inclusion : Meningococcal haemorrhagic adrenalitis;
Origin ID : 2072098125;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
A syndrome of the adrenal glands, commonly caused by an infection with meningococcus
Neisseria meningitidis. This syndrome is characterized by bleeding into the adrenal
glands due to the severe bacterial infection. This syndrome may present with fever,
chills, vomiting, myalgia, or rash, with progression to disseminated intravascular
coagulation. Transmission is by direct contact or droplet transmission.