ICD-11 code : 1C1C.1;
Preferred Label : Waterhouse-Friderichsen syndrome;
ICD-11 definition : A syndrome characterised by adrenal insufficiency due to bleeding into the adrenal
glands (mostly bilateral but sometimes also unilateral) due to the severe infection,
commonly caused by an infection with meningococcus (Neisseria meningitidis). However,
it can also be caused by infections with other bacteria such as Streptococcus pneumoniae
or Haemophilus influenzae or even due to some severe viral infections. This syndrome
may present with fever, chills, vomiting, myalgia, or rash, with progression to disseminated
intravascular coagulation. Transmission of the underlying infections is by direct
contact or droplet transmission.;
ICD-11 synonym : meningococcal haemorrhagic adrenalitis; meningococcal adrenal syndrome; acute adrenal insufficiency with meningococcal septicaemia; haemorrhagic meningococcal adrenitis; meningococcal Waterhouse-Friderichsen syndrome; Meningococcal haemorrhagic adrenalitis; adrenal haemorrhage syndrome;
ICD-11 inclusion : meningococcal haemorrhagic adrenalitis;
Origin ID : 2072098125;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
A syndrome characterised by adrenal insufficiency due to bleeding into the adrenal
glands (mostly bilateral but sometimes also unilateral) due to the severe infection,
commonly caused by an infection with meningococcus (Neisseria meningitidis). However,
it can also be caused by infections with other bacteria such as Streptococcus pneumoniae
or Haemophilus influenzae or even due to some severe viral infections. This syndrome
may present with fever, chills, vomiting, myalgia, or rash, with progression to disseminated
intravascular coagulation. Transmission of the underlying infections is by direct
contact or droplet transmission.
