ICD-11 code : LB17.3;
Preferred Label : Cloacal exstrophy;
ICD-11 definition : Rare and complex anorectal and genitourinary malformation in which rectum, vagina
and urinary tract share a common everted orifice, accompanied by an omphalocele and
an imperforate anus. Exstrophy of the cloaca is a well-known malformation that includes
the persistence and the exstrophy of a cloaca that receives ureters, ileum and a rudimentary
hindgut. Cloacal exstrophy is a severe birth defect wherein much of the abdominal
organs (the bladder and intestines) are exposed. It often causes the splitting of
both male and female feitalia (specifically, the penis and clitoris respectively),
and the anus is occasionally sealed.;
Origin ID : 2004612103;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Rare and complex anorectal and genitourinary malformation in which rectum, vagina
and urinary tract share a common everted orifice, accompanied by an omphalocele and
an imperforate anus. Exstrophy of the cloaca is a well-known malformation that includes
the persistence and the exstrophy of a cloaca that receives ureters, ileum and a rudimentary
hindgut. Cloacal exstrophy is a severe birth defect wherein much of the abdominal
organs (the bladder and intestines) are exposed. It often causes the splitting of
both male and female feitalia (specifically, the penis and clitoris respectively),
and the anus is occasionally sealed.
