" /> Dementia due to Alzheimer disease with early onset - CISMeF





ICD-11 code : 6D80.0;

Preferred Label : Dementia due to Alzheimer disease with early onset;

ICD-11 definition : Dementia due to Alzheimer disease in which symptoms emerge before the age of 65 years. It is relatively rare, representing less than 5% of all cases, and may be genetically determined (autosomal dominant Alzheimer disease). Clinical presentation may be similar to cases with later onset, but a significant proportion of cases manifest atypical symptoms, with relatively less severe memory deficits.;

ICD-11 synonym : dementia in Alzheimer disease with early onset; early onset Alzheimer dementia; primary degenerative Alzheimer type dementia, presenile onset, uncomplicated; early onset Alzheimer type dementia, uncomplicated; Alzheimer disease dementia with early onset; dementia in Alzheimer disease type 2; primary degenerative Alzheimer type dementia, early onset; Alzheimer type presenile dementia;

ICD-11 inclusion : presenile brain sclerosis; presenile Alzheimer brain sclerosis; presenile sclerosis;

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Dementia due to Alzheimer disease in which symptoms emerge before the age of 65 years. It is relatively rare, representing less than 5% of all cases, and may be genetically determined (autosomal dominant Alzheimer disease). Clinical presentation may be similar to cases with later onset, but a significant proportion of cases manifest atypical symptoms, with relatively less severe memory deficits.

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27/07/2025


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