ICD-11 code : 6D80.0;
Preferred Label : Dementia due to Alzheimer disease with early onset;
ICD-11 definition : Dementia due to Alzheimer disease in which symptoms emerge before the age of 65 years.
It is relatively rare, representing less than 5% of all cases, and may be genetically
determined (autosomal dominant Alzheimer disease). Clinical presentation may be similar
to cases with later onset, but a significant proportion of cases manifest atypical
symptoms, with relatively less severe memory deficits.;
ICD-11 synonym : dementia in Alzheimer disease with early onset; early onset Alzheimer dementia; primary degenerative Alzheimer type dementia, presenile onset, uncomplicated; early onset Alzheimer type dementia, uncomplicated; Alzheimer disease dementia with early onset; dementia in Alzheimer disease type 2; primary degenerative Alzheimer type dementia, early onset; Alzheimer type presenile dementia;
ICD-11 inclusion : presenile brain sclerosis; presenile Alzheimer brain sclerosis; presenile sclerosis;
Origin ID : 199015879;
UMLS CUI : C0750901;
Currated CISMeF NLP mapping
Semantic type(s)
UMLS correspondences (same concept)
Dementia due to Alzheimer disease in which symptoms emerge before the age of 65 years.
It is relatively rare, representing less than 5% of all cases, and may be genetically
determined (autosomal dominant Alzheimer disease). Clinical presentation may be similar
to cases with later onset, but a significant proportion of cases manifest atypical
symptoms, with relatively less severe memory deficits.