" /> Endocardial fibroelastosis - CISMeF





ICD-11 code : BC43.3;

Preferred Label : Endocardial fibroelastosis;

ICD-11 definition : Endocardial fibroelastosis is a disorder of fetuses and infants of unclear etiology that is characterized by deposition of collargen and elastin, leading to ventricular hypertrophy and diffuse endocardial thickening. Causes are incompletely (especially mumps), metabolic disorder, autoimmune disease, and congenital left-sided obstructive lesion.;

ICD-11 synonym : endomyocardial fibroelastosis; elastomyofibrosis; EFE - [endocardial fibroelastosis];

ICD-11 acronym : EFE;

ICD-11 inclusion : congenital endocarditis; fibroelastosis; congenital subendocardial sclerosis; chronic congenital endocarditis; congenital endocardial fibroelastosis; congenital valvular endocarditis; congenital nonbacterial thrombotic endocarditis; primary endocardial fibroelastosis; congenital familial cardiomyopathy; fetal endocarditis; Congenital cardiomyopathy; fibroelastosis cordis;

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Endocardial fibroelastosis is a disorder of fetuses and infants of unclear etiology that is characterized by deposition of collargen and elastin, leading to ventricular hypertrophy and diffuse endocardial thickening. Causes are incompletely (especially mumps), metabolic disorder, autoimmune disease, and congenital left-sided obstructive lesion.

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05/05/2025


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