ICD-11 code : BC43.3;
Preferred Label : Endocardial fibroelastosis;
ICD-11 definition : Endocardial fibroelastosis is the formation of a marked fibro-elastic thickening of
the subendocardium in one or both cardiac ventricles. A disorder of fetuses and infants,
secondary causes include congenital left-sided obstructive cardiac lesions, metabolic
disorders, autoimmune disease (anti-Ro/anti-La antibodies), and transplacental viral
infection such as mumps. Primary endocardial fibroelastosis has been linked to recessive
and x-linked inheritance, such as with Barth syndrome.;
ICD-11 synonym : endomyocardial fibroelastosis; elastomyofibrosis; EFE - [endocardial fibroelastosis];
ICD-11 acronym : EFE;
ICD-11 inclusion : congenital endocarditis; fibroelastosis; congenital subendocardial sclerosis; chronic congenital endocarditis; congenital endocardial fibroelastosis; congenital valvular endocarditis; congenital nonbacterial thrombotic endocarditis; primary endocardial fibroelastosis; congenital familial cardiomyopathy; fetal endocarditis; Congenital cardiomyopathy; fibroelastosis cordis;
Origin ID : 1971033419;
UMLS CUI : C0014117;
Currated CISMeF NLP mapping
- ICD-10 Mapping
- See also inter- (CISMeF)
- Semantic type(s)
- UMLS correspondences (same concept)
Endocardial fibroelastosis is the formation of a marked fibro-elastic thickening of
the subendocardium in one or both cardiac ventricles. A disorder of fetuses and infants,
secondary causes include congenital left-sided obstructive cardiac lesions, metabolic
disorders, autoimmune disease (anti-Ro/anti-La antibodies), and transplacental viral
infection such as mumps. Primary endocardial fibroelastosis has been linked to recessive
and x-linked inheritance, such as with Barth syndrome.
