ICD-11 code : LB15.1;
Preferred Label : Atresia of small intestine;
ICD-11 definition : Jejunoileal atresias and stenoses are major causes of neonatal intestinal obstruction.
Atresia refers to a congenital obstruction with complete occlusion of the intestinal
lumen. It accounts for 95% of obstructions. Four types of jejunoileal atresias are
described. They can range from having a small area of blockage or web to missing large
sections of the intestines. Intestinal atresia is one of the most frequent causes
of bowel obstruction in the newborn. The ileal atresia is more common than jejunal
atresia, and multiple foci are more common than isolated atresia. The most accepted
theory regarding the etiology of jejunoileal atresia is that of an intrauterine vascular
accident resulting in necrosis of the affected segment. Stenosis, on the other hand,
refers to a partial occlusion with incomplete obstruction and accounts for the remaining
5% of cases. A stenosis has an intact mesentery and is a localized narrowing of the
bowel. No loss of continuity of the lumen exists.;
ICD-11 synonym : congenital small intestinal stricture NOS; Congenital stenosis of small intestine; Congenital absence of small intestine;
ICD-11 inclusion : Congenital absence of small intestine; Congenital stenosis of small intestine;
Origin ID : 1949256262;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
Jejunoileal atresias and stenoses are major causes of neonatal intestinal obstruction.
Atresia refers to a congenital obstruction with complete occlusion of the intestinal
lumen. It accounts for 95% of obstructions. Four types of jejunoileal atresias are
described. They can range from having a small area of blockage or web to missing large
sections of the intestines. Intestinal atresia is one of the most frequent causes
of bowel obstruction in the newborn. The ileal atresia is more common than jejunal
atresia, and multiple foci are more common than isolated atresia. The most accepted
theory regarding the etiology of jejunoileal atresia is that of an intrauterine vascular
accident resulting in necrosis of the affected segment. Stenosis, on the other hand,
refers to a partial occlusion with incomplete obstruction and accounts for the remaining
5% of cases. A stenosis has an intact mesentery and is a localized narrowing of the
bowel. No loss of continuity of the lumen exists.
