ICD-11 code : LA30.6;
Preferred Label : Amelogenesis imperfecta;
ICD-11 definition : Amelogenesis imperfecta presents with a rare abnormal formation of the enamel or external
layer of the crown of teeth. Amelogenesis imperfecta is due to the malfunction of
the proteins in the enamel: ameloblastin, enamelin, tuftelin and amelogenin. People
afflicted with amelogenesis imperfecta have teeth with abnormal color: yellow, brown
or grey; this disorder can afflict any number of teeth of both dentitions. The teeth
have a higher risk for dental cavities and are hypersensitive to temperature changes
as well as rapid attrition, excessive calculus deposition, and gingival hyperplasia.;
ICD-11 inclusion : hypominerlisation amelogenesis imperfecta;
Origin ID : 1923123066;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Amelogenesis imperfecta presents with a rare abnormal formation of the enamel or external
layer of the crown of teeth. Amelogenesis imperfecta is due to the malfunction of
the proteins in the enamel: ameloblastin, enamelin, tuftelin and amelogenin. People
afflicted with amelogenesis imperfecta have teeth with abnormal color: yellow, brown
or grey; this disorder can afflict any number of teeth of both dentitions. The teeth
have a higher risk for dental cavities and are hypersensitive to temperature changes
as well as rapid attrition, excessive calculus deposition, and gingival hyperplasia.
