ICD-11 definition : Haemophilia B is a form of haemophilia characterised by spontaneous or prolonged haemorrhages
due to factor IX deficiency. Depending on the extent of the factor IX deficiency,
it can be severe (biological activity of factor IX below 1%), moderately severe (activity
of factor IX between 1% and 5%), or mild (activity of factor IX between 5 and 40%).;
Haemophilia B is a form of haemophilia characterised by spontaneous or prolonged haemorrhages
due to factor IX deficiency. Depending on the extent of the factor IX deficiency,
it can be severe (biological activity of factor IX below 1%), moderately severe (activity
of factor IX between 1% and 5%), or mild (activity of factor IX between 5 and 40%).