ICD-11 code : 3B14.1;
Preferred Label : Hereditary factor X deficiency;
ICD-11 definition : Congenital factor X deficiency is an inherited bleeding disorder with a decreased
antigen and/or activity of factor X (FX) and characterized by mild to severe bleeding
symptoms.;
ICD-11 synonym : Stuart-Prower factor deficiency; Congenital Stuart factor deficiency;
ICD-11 inclusion : congenital factor x deficiency; Stuart deficiency disease; Stuart-Prower disease; Stuart Prower deficiency; Deficiency of factor X;
Origin ID : 1886781445;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
Congenital factor X deficiency is an inherited bleeding disorder with a decreased
antigen and/or activity of factor X (FX) and characterized by mild to severe bleeding
symptoms.