" /> Hereditary factor X deficiency - CISMeF





ICD-11 code : 3B14.1;

Preferred Label : Hereditary factor X deficiency;

ICD-11 definition : Congenital factor X deficiency is an inherited bleeding disorder with a decreased antigen and/or activity of factor X (FX) and characterized by mild to severe bleeding symptoms.;

ICD-11 synonym : Stuart-Prower factor deficiency; Congenital Stuart factor deficiency;

ICD-11 inclusion : congenital factor x deficiency; Stuart deficiency disease; Stuart-Prower disease; Stuart Prower deficiency; Deficiency of factor X;

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Congenital factor X deficiency is an inherited bleeding disorder with a decreased antigen and/or activity of factor X (FX) and characterized by mild to severe bleeding symptoms.

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29/07/2025


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