Limited systemic sclerosis

ICD-11 code : 4A42.2;

Preferred Label : Limited systemic sclerosis;

ICD-11 definition : Combination of calcinosis, Raynaud phenomenon, (o)esophageal dysfunction, sclerodactyly and telangiectasia.;

ICD-11 synonym : CRST - [calcinosis, Raynaud phenomenon, sclerodactyly and telangiectasia] syndrome; CRST syndrome; CREST - [calcinosis, Raynaud phenomenon, oesophageal dysmotility, sclerodactyly, and telangiectasia] syndrome; CREST syndrome;

Details

Origin ID

187455179;

Automatic exact mappings (from CISMeF team)
- CRST syndrome [MeSH concept]
- CRST syndrome [MedDRA LLT]
- Calcinosis, Raynaud's phenomenon, sclerodactyly, and telangiectasia syndrome (disorder) [SNOMED CT concept]
- Scleroderma, familial progressive [OMIM Phenotype]
- crst syndrome [SNOMED Notion]
Currated CISMeF NLP mapping
- CREST Syndrome [NCIt concept]
- CREST syndrome [MeSH Descriptor]
- CREST syndrome [MeSH concept]
- CREST syndrome [MedDRA Preferred Term]
- CREST syndrome [ORDO Disease]
- CREST syndrome [DO Concept]
- CREST syndrome [PASCAL descriptor]
- Calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia syndrome (disorder) [SNOMED CT concept]
- Limited systemic sclerosis [ORDO Disease]
- Limited systemic sclerosis (disorder) [SNOMED CT concept]
- crest syndrome [SNOMED Notion]
- limited scleroderma [DO Concept]
ICD-10 Mapping
- CR(E)ST syndrome [ICD-10 Sub-category]
See also inter- (CISMeF)
- CR(E)ST syndrome [ICD-10 Sub-category (who)]

Keyword's position in hierarchy(ies) :

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