ICD-11 code : 4A42.1;
Preferred Label : Diffuse systemic sclerosis;
ICD-11 definition : Diffuse cutaneous systemic sclerosis (dcSSc) is a subtype of Systemic Sclerosis (SSc)
characterized by truncal and acral skin fibrosis with an early and significant incidence
of diffuse involvement (interstitial lung disease, oliguric renal failure, diffuse
gastrointestinal disease, and myocardial involvement).;
ICD-11 synonym : Progressive system sclerosis;
Origin ID : 1852283743;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Diffuse cutaneous systemic sclerosis (dcSSc) is a subtype of Systemic Sclerosis (SSc)
characterized by truncal and acral skin fibrosis with an early and significant incidence
of diffuse involvement (interstitial lung disease, oliguric renal failure, diffuse
gastrointestinal disease, and myocardial involvement).