ICD-11 code : LA89.3;
Preferred Label : Hypoplastic left heart syndrome;
ICD-11 definition : A spectrum of congenital cardiovascular malformations with normally aligned great
arteries without a common atrioventricular junction, characterised by underdevelopment
of the left heart with significant hypoplasia of the left ventricle including atresia,
stenosis, or hypoplasia of the aortic or mitral valve, or both valves, and hypoplasia
of the ascending aorta and aortic arch.;
ICD-11 synonym : left heart hypoplasia syndrome; hypoplasia of the left heart; HLHS - [hypoplastic left heart syndrome];
ICD-11 acronym : HLHS;
ICD-11 inclusion : atresia of mitral valve, in hypoplastic left heart syndrome; hypoplasia of aortic valve, in hypoplastic left heart syndrome; ascending aorta hypoplasia, in hypoplastic left heart syndrome; aortic valve atresia, in hypoplastic left heart syndrome; atresia or marked hypoplasia, of aortic orifice or valve, with hypoplasia of ascending
aorta and defective development of left ventricle with mitral valve atresia; atresia or marked hypoplasia of aortic orifice or valve, with hypoplasia of ascending
aorta and defective development of left ventricle;
Origin ID : 1811800027;
Currated CISMeF NLP mapping
- ICD-10 Mapping
- Validated automatic mappings to BTNT
A spectrum of congenital cardiovascular malformations with normally aligned great
arteries without a common atrioventricular junction, characterised by underdevelopment
of the left heart with significant hypoplasia of the left ventricle including atresia,
stenosis, or hypoplasia of the aortic or mitral valve, or both valves, and hypoplasia
of the ascending aorta and aortic arch.
