ICD-11 code : CA27.0;
Preferred Label : Tracheobronchopathia osteochondroplastica;
ICD-11 definition : Tracheobronchopathia osteochondroplastica is a rare disorder of unknown cause, seen
with a frequency of 0.4 percent at bronchoscopy, affecting the large airways. It is
characterized by the development of multiple osseous and cartilaginous submucosal
nodules connected to tracheal cartilage. The abnormality spares the posterior tracheal
membranous wall. In spite of marked radiographic changes, patients are only rarely
symptomatic since severe airway obstruction is unusual. Linear tracheoplasty may be
required in patients with symptomatic airway obstruction.;
Origin ID : 1797446244;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Tracheobronchopathia osteochondroplastica is a rare disorder of unknown cause, seen
with a frequency of 0.4 percent at bronchoscopy, affecting the large airways. It is
characterized by the development of multiple osseous and cartilaginous submucosal
nodules connected to tracheal cartilage. The abnormality spares the posterior tracheal
membranous wall. In spite of marked radiographic changes, patients are only rarely
symptomatic since severe airway obstruction is unusual. Linear tracheoplasty may be
required in patients with symptomatic airway obstruction.
