ICD-11 code : 8B22.B;
Preferred Label : Moyamoya syndrome;
ICD-11 definition : A cerebrovascular disease caused by stenotic arteries at the base of the brain in
the basal ganglia. Moyamoya, meaning puff of smoke refers to the appearance of the
anastomotic vessel network formed at the base of the brain distal to the circle of
Willis to compensate for the blockage.;
Origin ID : 1746892088;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
A cerebrovascular disease caused by stenotic arteries at the base of the brain in
the basal ganglia. Moyamoya, meaning puff of smoke refers to the appearance of the
anastomotic vessel network formed at the base of the brain distal to the circle of
Willis to compensate for the blockage.