ICD-11 code : 2A85.0;
Preferred Label : Nodal marginal zone lymphoma;
ICD-11 definition : A primary nodal B-cell non-Hodgkin lymphoma which morphologically resembles lymph
nodes involved by marginal zone lymphomas of extranodal or splenic types, but without
evidence of extranodal or splenic disease. This is a rare entity, and most patients
present with localized or generalized lymphadenopathy. The clinical course is indolent.;
Origin ID : 1720785883;
Automatic exact mappings (from CISMeF team)
A primary nodal B-cell non-Hodgkin lymphoma which morphologically resembles lymph
nodes involved by marginal zone lymphomas of extranodal or splenic types, but without
evidence of extranodal or splenic disease. This is a rare entity, and most patients
present with localized or generalized lymphadenopathy. The clinical course is indolent.