ICD-11 code : 9C82.0;
Preferred Label : Progressive external ophthalmoplegia;
ICD-11 definition : Chronic ophthalmoplegia is characterized by progressive weakness of ocular muscles
and levator muscle of the upper eyelid. The condition is mainly manifested in adults.
It may be totally and permanently isolated, however in a minority of cases it is associated
with skeletal myopathy, which causes abnormal fatigability and even permanent muscle
weakness. In this case the affection is still termed isolated progressive external
ophthalmoplegia. A large proportion of chronic ophthalmoplegias presents with multisystemic
pattern of signs: neurological signs (hearing loss, retinopathy, cerebellar disorders,
peripheral neuropathy, etc.), endocrine (diabetes, hypogonadism, hypoparathyroidism,
etc.), kidney (kidney failure, tubulopathy, etc.), and heart disorders (conduction
disorders, myocardiopathy, etc.).;
ICD-11 synonym : Graefe disease; PEO - [progressive external ophthalmoplegia];
ICD-11 acronym : PEO;
Origin ID : 1698427219;
UMLS CUI : C0162674;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
- Semantic type(s)
- UMLS correspondences (same concept)
Chronic ophthalmoplegia is characterized by progressive weakness of ocular muscles
and levator muscle of the upper eyelid. The condition is mainly manifested in adults.
It may be totally and permanently isolated, however in a minority of cases it is associated
with skeletal myopathy, which causes abnormal fatigability and even permanent muscle
weakness. In this case the affection is still termed isolated progressive external
ophthalmoplegia. A large proportion of chronic ophthalmoplegias presents with multisystemic
pattern of signs: neurological signs (hearing loss, retinopathy, cerebellar disorders,
peripheral neuropathy, etc.), endocrine (diabetes, hypogonadism, hypoparathyroidism,
etc.), kidney (kidney failure, tubulopathy, etc.), and heart disorders (conduction
disorders, myocardiopathy, etc.).
