" /> Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated - CISMeF





ICD-11 code : 2A90.5;

Preferred Label : Adult T-cell lymphoma or leukaemia, human T-cell lymphotropic virus type 1-associated;

ICD-11 definition : A peripheral (mature) T-cell neoplasm linked to the human T-cell leukemia virus type 1 (HTLV-1). Adult T-cell leukemia/lymphoma is endemic in several regions of the world, in particular Japan, the Caribbean, and parts of Central Africa.;

ICD-11 synonym : adult t-cell leukaemia; adult t-cell leukaemia/lymphoma HTLV-1; adult t-cell leukaemia/lymphoma HTLV-1 - [human t-cell lymphotropic virus type 1 positive]; adult t-cell lymphoma; adult t cell leukaemia lymphoma; adult t-cell lymphoma/leukaemia (htlv-1-associated), NOS; adult t-cell leukaemia/lymphoma (htlv-1 positive); human t-cell lymphotropic virus type 1 positive; adult t-cell leukaemia/lymphoma;

ICD-11 inclusion : Chronic variant of adult T-cell lymphoma/leukaemia; adult T-cell lymphoma/leukaemia (HTLV-1-associated) without mention of remission; pro-T ALL; Smouldering variant of adult T-cell lymphoma/leukaemia; precursor t-cell lymphoblastic leukaemia; Acute variant of adult T-cell lymphoma/leukaemia; Lymphomatoid variant of adult T-cell lymphoma/leukaemia; t-cell acute lymphoblastic leukaemia; cortical T ALL; pre-T ALL;

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A peripheral (mature) T-cell neoplasm linked to the human T-cell leukemia virus type 1 (HTLV-1). Adult T-cell leukemia/lymphoma is endemic in several regions of the world, in particular Japan, the Caribbean, and parts of Central Africa.

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31/07/2025


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