ICD-11 definition : Lichen sclerosus of the vulva is an inflammatory disorder of unknown aetiology affecting
the skin of the vulva and perianal area. Typically it affects women in the fifth and
sixth decades of life though is not uncommon in prepubertal girls. It presents with
pruritus, soreness or dyspareunia. The affected skin is white and atrophic, though
secondary changes including maceration, purpura and erosion may dominate the clinical
picture. In longstanding cases there may be marked shrinkage of the vulva, labial
fusion and an increased risk of malignant transformation.;
ICD-11 synonym : Lichen sclerosus et atrophicus of vulva; Vulval lichen sclerosus; Kraurosis vulvae;
Lichen sclerosus of the vulva is an inflammatory disorder of unknown aetiology affecting
the skin of the vulva and perianal area. Typically it affects women in the fifth and
sixth decades of life though is not uncommon in prepubertal girls. It presents with
pruritus, soreness or dyspareunia. The affected skin is white and atrophic, though
secondary changes including maceration, purpura and erosion may dominate the clinical
picture. In longstanding cases there may be marked shrinkage of the vulva, labial
fusion and an increased risk of malignant transformation.