ICD-11 code : 5C90.3;
Preferred Label : Liver disease due to disorders of lysosomal storage;
ICD-11 definition : This is liver disease due to a group of approximately 50 rare inherited metabolic
disorders that result from defects in lysosomal function.;
Origin ID : 1600152465;
ICD-10 Mapping
Validated automatic mappings to NTBT
This is liver disease due to a group of approximately 50 rare inherited metabolic
disorders that result from defects in lysosomal function.