ICD-11 code : 7A42.0;
Preferred Label : Obesity hypoventilation syndrome;
ICD-11 definition : Extreme obesity associated with alveolar hypoventilation; a Pickwickian syndrome[1]
is a breathing disorder that affects some obese people. Poor breathing results in
too much carbon dioxide (hypoventilation) and too little oxygen in the blood (hypoxemia).
These changes can lead to serious health problems, such as leg edema, pulmonary hypertension,
cor pulmonale, and secondary erythrocytosis(Obesity hypoventilation syndrome :OHS).
If left untreated, OHS can even be fatal. Many people who have OHS also have obstructive
sleep apnea. [2] The central features of OHS, as currently accepted, include obesity
(BMI 30 kg/m2), chronic alveolar hypoventilation leading to daytime hypercapnia and
hypoxia (PaCO2 45 mm Hg and PaO2 70 mm Hg), and sleep-disordered breathing. Essential
to the diagnosis is exclusion of other causes of alveolar hypoventilation such as
severe obstructive or restrictive pulmonary disease, significant kyphoscoliosis, severe
hypothyroidism, neuromuscular diseases, or other central hypoventilation syndromes.[3];
ICD-11 synonym : OHS - [obesity hypoventilation syndrome]; alveolar hypoventilation syndrome; cardiopulmonary obesity syndrome; alveolus hypoventilation syndrome; Pickwickian syndrome; Extreme obesity with alveolar hypoventilation with Body-Mass-Index unspecified;
ICD-11 acronym : OHS;
ICD-11 inclusion : Pickwickian syndrome;
Origin ID : 1514276050;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Extreme obesity associated with alveolar hypoventilation; a Pickwickian syndrome[1]
is a breathing disorder that affects some obese people. Poor breathing results in
too much carbon dioxide (hypoventilation) and too little oxygen in the blood (hypoxemia).
These changes can lead to serious health problems, such as leg edema, pulmonary hypertension,
cor pulmonale, and secondary erythrocytosis(Obesity hypoventilation syndrome :OHS).
If left untreated, OHS can even be fatal. Many people who have OHS also have obstructive
sleep apnea. [2] The central features of OHS, as currently accepted, include obesity
(BMI 30 kg/m2), chronic alveolar hypoventilation leading to daytime hypercapnia and
hypoxia (PaCO2 45 mm Hg and PaO2 70 mm Hg), and sleep-disordered breathing. Essential
to the diagnosis is exclusion of other causes of alveolar hypoventilation such as
severe obstructive or restrictive pulmonary disease, significant kyphoscoliosis, severe
hypothyroidism, neuromuscular diseases, or other central hypoventilation syndromes.[3]