ICD-11 code : 3B14.0;
Preferred Label : Hereditary deficiency of factor I;
ICD-11 definition : Congenital deficiencies of fibrinogen are coagulation disorders characterized by bleeding
symptoms ranging from mild to severe resulting from reduced quantity and/or quality
of circulating fibrinogen. Afibrinogenemia (complete absence of fibrinogen) and hypofibrinogenemia
(reduced plasma fibrinogen concentration) correspond to quantitative anomalies of
fibrinogen while dysfibrinogenemia corresponds to a functional anomaly of fibrinogen.
Hypo- and dysfibrinogenemia may be frequently combined (hypodysfibrinogenemia).;
ICD-11 inclusion : Deficiency of factor 1; Hereditary fibrinogen deficiency; congenital fibrinogenopenia; Deficiency of fibrinogen;
Origin ID : 1452989457;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Congenital deficiencies of fibrinogen are coagulation disorders characterized by bleeding
symptoms ranging from mild to severe resulting from reduced quantity and/or quality
of circulating fibrinogen. Afibrinogenemia (complete absence of fibrinogen) and hypofibrinogenemia
(reduced plasma fibrinogen concentration) correspond to quantitative anomalies of
fibrinogen while dysfibrinogenemia corresponds to a functional anomaly of fibrinogen.
Hypo- and dysfibrinogenemia may be frequently combined (hypodysfibrinogenemia).
