ICD-11 definition : Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation
of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur
in association with systemic disease. Clinical forms include cutaneous mastocytoma,
urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous
mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.;
Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation
of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur
in association with systemic disease. Clinical forms include cutaneous mastocytoma,
urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous
mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.