Budd-Chiari syndrome

ICD-11 code : DB98.5;

Preferred Label : Budd-Chiari syndrome;

ICD-11 definition : Budd-Chiari syndrome is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava and leading to hepatic congestion and ischemic necrosis. Severity depends on the speed of onset and extent of the obstruction. Obstructions are generally caused by thrombosis in primary BCS, while secondary BCS results from tumour invasion into the lumen or compression of the vein by an expansive lesion. The principle manifestations of BCS are ascites leading to undernutrition and renal insufficiency, gastrointestinal haemorrhage due to portal hypertension, and hepatic insufficiency resulting in encephalopathy and severe infections. Asymptomatic forms have also been reported.;

ICD-11 synonym : Chiari syndrome; obstruction of hepatic veins; hepatic vein block;

ICD-11 inclusion : Budd-Chiari syndrome with hepatic thrombosis; liver thrombosis; hepatic venous embolism; Budd-Chiari syndrome with hepatic vein embolism; hepatic venous thrombosis; hepatic vein obstruction; Budd-Chiari syndrome with hepatic vein thrombosis; hepatic venous block; Budd-Chiari syndrome with hepatic embolism;

Details

Origin ID

1300118676;

UMLS CUI

C0856761;

Automatic exact mappings (from CISMeF team)
- Budd-Chiari Syndrome, CTCAE [NCIt concept]
- Hepatic vein obstruction [MedDRA LLT]
Currated CISMeF NLP mapping
- BUDD CHIARI SYNDROME [WHO-ART Preferred Term]
- Budd Chiari syndrome [MedDRA LLT]
- Budd-Chiari syndrome [HPO term]
- Budd-Chiari syndrome [PASCAL descriptor]
- Budd-Chiari syndrome [Radlex concept]
- Budd-Chiari syndrome [MeSH concept]
- Budd-Chiari syndrome [MedDRA Preferred Term]
- Budd-Chiari syndrome [ORDO Disease]
- Budd-Chiari syndrome [DO Concept]
- Budd-Chiari syndrome [ICD-10 Sub-category]
- Budd-Chiari syndrome [ICD-10 Sub-category (who)]
- Budd-Chiari syndrome (disorder) [SNOMED CT concept]
- Budd-chiari syndrome [ICD-9 code]
- Budd-chiari syndrome [OMIM Phenotype]
- Hepatic vein thrombosis [MedDRA Preferred Term]
- Hepatic vein thrombosis (disorder) [SNOMED CT concept]
- Syndrome Budd-Chiari [MedDRA LLT]
- budd-chiari syndrome [SNOMED Notion]
- budd-chiari syndrome [MeSH Descriptor]
- liver vein thrombosis [Disease (Nov.)]
ICD-10 Mapping
- Budd-Chiari syndrome [ICD-10 Sub-category]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- BUDD CHIARI SYNDROME [WHO-ART Preferred Term]
- Budd Chiari syndrome [MedDRA LLT]
- Budd-Chiari syndrome [HPO term]
- Budd-Chiari syndrome [ICD-10 Sub-category]
- Budd-Chiari syndrome [MedDRA Preferred Term]
- Budd-Chiari syndrome [MeSH concept]
- Budd-Chiari syndrome (disorder) [SNOMED CT concept]
- Budd-chiari syndrome [ICD-9 code]
- Budd-chiari syndrome [OMIM Phenotype]
- Hepatic vein obstruction [MedDRA LLT]
- Hepatic venous outflow obstruction [MedDRA LLT]
- Syndrome Budd-Chiari [MedDRA LLT]
- budd-chiari syndrome [MeSH Descriptor]
- budd-chiari syndrome [SNOMED Notion]

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