ICD-11 code : CB22.0;
Preferred Label : Fibrosing mediastinitis;
ICD-11 definition : Fibrosing mediastinitis, also known as sclerosing mediastinitis or mediastinal fibrosis,
is a disorder characterized by an excessive fibrotic reaction in the mediastinum.
It can result in compromise of airways, great vessels, and other mediastinal structures,
with morbidity directly related to the location and extent of fibrosis. The commonest
cause is histoplasmosis, of which it is a rare late complication, but it may also
occur in association with other infections and with systemic autoimmune disorders
such as Behçet disease, granulomatosis with polyangiitis and retoperitoneal fibrosis.;
ICD-11 synonym : mediastinal fibrosis;
ICD-11 inclusion : idiopathic mediastinal fibrosis; fibrosing mediastinitis in association with systemic autoimmune disease;
Origin ID : 123840075;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Fibrosing mediastinitis, also known as sclerosing mediastinitis or mediastinal fibrosis,
is a disorder characterized by an excessive fibrotic reaction in the mediastinum.
It can result in compromise of airways, great vessels, and other mediastinal structures,
with morbidity directly related to the location and extent of fibrosis. The commonest
cause is histoplasmosis, of which it is a rare late complication, but it may also
occur in association with other infections and with systemic autoimmune disorders
such as Behçet disease, granulomatosis with polyangiitis and retoperitoneal fibrosis.
