ICD-11 definition : A congenital disorder of ventricular myocardial repolarization characterized by a
prolonged QT interval on the electrocardiogram (ECG) that can lead to symptomatic
ventricular arrhythmias and an increased risk of sudden cardiac death.;
ICD-11 synonym : Congenital long QT syndrome; Familial long QT syndrome;
A congenital disorder of ventricular myocardial repolarization characterized by a
prolonged QT interval on the electrocardiogram (ECG) that can lead to symptomatic
ventricular arrhythmias and an increased risk of sudden cardiac death.