" /> Long QT syndrome - CISMeF





ICD-11 code : BC65.0;

Preferred Label : Long QT syndrome;

ICD-11 definition : A congenital disorder of ventricular myocardial repolarization characterized by a prolonged QT interval on the electrocardiogram (ECG) that can lead to symptomatic ventricular arrhythmias and an increased risk of sudden cardiac death.;

ICD-11 synonym : Congenital long QT syndrome; Familial long QT syndrome;

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A congenital disorder of ventricular myocardial repolarization characterized by a prolonged QT interval on the electrocardiogram (ECG) that can lead to symptomatic ventricular arrhythmias and an increased risk of sudden cardiac death.

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28/07/2025


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