" /> Disorders of pyruvate metabolism - CISMeF





ICD-11 code : 5C53.0;

Preferred Label : Disorders of pyruvate metabolism;

ICD-11 synonym : disorders of pyruvate metabolism and gluconeogenesis;

ICD-11 inclusion : pyruvate dehydrogenase deficiency; ataxia with lactic acidosis 2; ataxia with lactic acidosis 1; gluconeogenesis disorder;

ICD-11 "other" category code : 5C53.0Y;

ICD-11 "unspecified" category code : 5C53.0Z;

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28/07/2025


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