Preferred Label : Phakomatosis pigmentokeratotica;
ICD-11 definition : Phacomatosis pigmentokeratotica is a rare syndrome defined by the association of an
organoid naevus (occasionally with sebaceous differentiation), a speckled lentiginous
naevus, and other extracutaneous anomalies.;
Origin ID : 960559196;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
Phacomatosis pigmentokeratotica is a rare syndrome defined by the association of an
organoid naevus (occasionally with sebaceous differentiation), a speckled lentiginous
naevus, and other extracutaneous anomalies.
