" /> Ectodermal dysplasia - acanthosis nigricans - CISMeF





Preferred Label : Ectodermal dysplasia - acanthosis nigricans;

ICD-11 definition : Lelis syndrome is characterised by the association of ectodermal dysplasia (hypotrichosis and hypohidrosis) with acanthosis nigricans.;

ICD-11 synonym : Lelis syndrome;

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Lelis syndrome is characterised by the association of ectodermal dysplasia (hypotrichosis and hypohidrosis) with acanthosis nigricans.

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27/07/2025


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