Preferred Label : Ehlers-Danlos syndrome, periodontitis type;
ICD-11 definition : Ehlers-Danlos syndrome, periodontitis type is a type of Ehlers-Danlos syndromes (EDS),a
heterogeneous group of hereditary connective tissue diseases characterized by joint
hyperlaxity, cutaneous hyperelasticity and tissue fragility, and is characterized
by severe early-onset periodontal disease in conjunction with the presence of plaques
of scar tissue in the pretibial zones (hyperpigmented atrophic scars).;
ICD-11 synonym : Ehlers-Danlos syndrome type 8;
Origin ID : 893527307;
Currated CISMeF NLP mapping
Ehlers-Danlos syndrome, periodontitis type is a type of Ehlers-Danlos syndromes (EDS),a
heterogeneous group of hereditary connective tissue diseases characterized by joint
hyperlaxity, cutaneous hyperelasticity and tissue fragility, and is characterized
by severe early-onset periodontal disease in conjunction with the presence of plaques
of scar tissue in the pretibial zones (hyperpigmented atrophic scars).
