ICD-11 definition : Scalp-ear-nipple syndrome is characterised by the following triad: areas of hairless
raw skin over the scalp (present at birth and healing during childhood), prominent,
hypoplastic ears with almost absent pinnae, and bilateral amastia.;
Scalp-ear-nipple syndrome is characterised by the following triad: areas of hairless
raw skin over the scalp (present at birth and healing during childhood), prominent,
hypoplastic ears with almost absent pinnae, and bilateral amastia.