Preferred Label : Early onset benign occipital epilepsy, Panayiotopoulos type;
ICD-11 definition : An epilepsy syndrome usually presenting in early childhood with focal seizures with
autonomic features, commonly vomiting, and motor features such as eye deviation. Seizures
are often prolonged. The EEG commonly shows stereotypic high amplitude focal spikes
and may be activated by sleep. Only 25% of cases have frequent seizures. Remission
usually occurs within a few years. An electroencephalogram is normal in 10% of patients.
In 90% of patients there are occipital spikes which often shift from one region to
another in sequential EEGs. A polygenetic cause is likely.;
ICD-11 synonym : Panayiotopoulos syndrome;
Origin ID : 821291892;
Automatic exact mappings (from CISMeF team)
An epilepsy syndrome usually presenting in early childhood with focal seizures with
autonomic features, commonly vomiting, and motor features such as eye deviation. Seizures
are often prolonged. The EEG commonly shows stereotypic high amplitude focal spikes
and may be activated by sleep. Only 25% of cases have frequent seizures. Remission
usually occurs within a few years. An electroencephalogram is normal in 10% of patients.
In 90% of patients there are occipital spikes which often shift from one region to
another in sequential EEGs. A polygenetic cause is likely.
