Preferred Label : CANOMAD - [Chronic sensory ataxic neuropathy with anti-dyalosyl IgM antibodies] syndrome;
ICD-11 definition : CANOMAD syndrome (Chronic Ataxic Neuropathy, Ophthalmoplegia, Monoclonal IgM protein,
cold Agglutinins and Disialosyl antibodies) is a rare chronic immune-mediated demyelinating
polyneuropathy with marked sensory ataxia and areflexia, and with relatively preserved
motor function in the limbs.;
ICD-11 synonym : CANOMAD syndrome; Chronic sensory ataxic neuropathy with anti-dyalosyl IgM antibodies;
Origin ID : 803014219;
Currated CISMeF NLP mapping
CANOMAD syndrome (Chronic Ataxic Neuropathy, Ophthalmoplegia, Monoclonal IgM protein,
cold Agglutinins and Disialosyl antibodies) is a rare chronic immune-mediated demyelinating
polyneuropathy with marked sensory ataxia and areflexia, and with relatively preserved
motor function in the limbs.