Preferred Label : Neutrophilic eccrine hidradenitis;
ICD-11 definition : Neutrophilic eccrine hidradenitis is an uncommon cutaneous eruption condition characterized
histologically by necrosis of the eccrine epithelium and eccrine secretory coil with
a dense surrounding neutrophilic infiltrate. The typical clinical presentation is
of solitary or disseminated purpuric macules, nodules or plaques arising on the limbs,
neck, face and ears 8–10 days after the start of chemotherapy for malignancy, especially
acute myeloid leukaemia. It is often associated with fever and may on occasion simulate
bacterial cellulitis. Although most commonly associated with chemotherapy, it has
been reported in association with infections in immunodeficient hosts and as a paraneoplastic
phenomenon.;
ICD-11 inclusion : Chemotherapy-associated neutrophilic eccrine hidradenitis; Idiopathic recurrent palmoplantar hidradenitis; Palmoplantar eccrine hidradenitis;
Origin ID : 789957175;
Automatic exact mappings (from CISMeF team)
Neutrophilic eccrine hidradenitis is an uncommon cutaneous eruption condition characterized
histologically by necrosis of the eccrine epithelium and eccrine secretory coil with
a dense surrounding neutrophilic infiltrate. The typical clinical presentation is
of solitary or disseminated purpuric macules, nodules or plaques arising on the limbs,
neck, face and ears 8–10 days after the start of chemotherapy for malignancy, especially
acute myeloid leukaemia. It is often associated with fever and may on occasion simulate
bacterial cellulitis. Although most commonly associated with chemotherapy, it has
been reported in association with infections in immunodeficient hosts and as a paraneoplastic
phenomenon.
