" /> Primary ciliary dyskinesia, Kartagener type - CISMeF





Preferred Label : Primary ciliary dyskinesia, Kartagener type;

ICD-11 definition : Primary ciliary diskinesia, Kartagener type is an autosomal recessive variant of primary cilia dyskinesia which associates respiratory disorders (chronic bronchorrhea with bronchoectasis and chronic sinusitis) with situs inversus. Men may present with infertility because of immotile sperm.;

ICD-11 synonym : Immotile cilia syndrome, Kartagener type; Kartagener syndrome; Siewert syndrome; Dextrocardia - bronchiectasis - sinusitis;

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Primary ciliary diskinesia, Kartagener type is an autosomal recessive variant of primary cilia dyskinesia which associates respiratory disorders (chronic bronchorrhea with bronchoectasis and chronic sinusitis) with situs inversus. Men may present with infertility because of immotile sperm.

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28/07/2025


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