Preferred Label : Bullous lichen planus;
ICD-11 definition : Bullous lichen planus is a variant of rare lichen planus characterized by the development
of vesico-bullous lesions. Prevalence is unknown and only a few cases, both sporadic
and familial, have been described in the literature. The disease manifests during
childhood or adolescence. Bullous lesions develop on top of preexisting lichen planus
papules or on normal skin and generally affect the lower limbs or the lower mucosal
lip, and in some rare cases the torso. In this condition, the epithelium separates
from the epidermis. In the case of oral bullous lichen planus, the vesicles and bullae
burst soon after they appear which results in erosions. Etiology is unknown.;
ICD-11 synonym : Lichen planus bullosus;
Origin ID : 606709958;
Automatic exact mappings (from CISMeF team)
Bullous lichen planus is a variant of rare lichen planus characterized by the development
of vesico-bullous lesions. Prevalence is unknown and only a few cases, both sporadic
and familial, have been described in the literature. The disease manifests during
childhood or adolescence. Bullous lesions develop on top of preexisting lichen planus
papules or on normal skin and generally affect the lower limbs or the lower mucosal
lip, and in some rare cases the torso. In this condition, the epithelium separates
from the epidermis. In the case of oral bullous lichen planus, the vesicles and bullae
burst soon after they appear which results in erosions. Etiology is unknown.