" /> Peripubertal primary lymphoedema - CISMeF





Preferred Label : Peripubertal primary lymphoedema;

ICD-11 definition : Lymphoedema presenting after birth and before age 35, usually at puberty;

ICD-11 synonym : Hereditary lymphoedema type II: (MIM153200); Lymphoedema praecox; Meige disease; Hereditary lymphoedema type II:;

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Lymphoedema presenting after birth and before age 35, usually at puberty

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24/07/2025


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