Preferred Label : Sclerodactyly;
ICD-11 definition : Sclerodactyly is a morphological term used to describe thickening and sclerosis of
the skin and soft tissues of the fingers with resultant limitation of movement and
joint contractures. In severe cases ulceration may occur. It is typically seen in
autoimmune disorders including limited systemic sclerosis (CRST syndrome), diffuse
systemic sclerosis and mixed connective tissue disease, in which case it is likely
to be associated with Raynaud phenomenon. It may also be associated, however, with
long-standing diabetes (diabetic cheiroarthropathy), exposure to certain drugs and
or chemicals, in hand-arm vibration syndrome and in a number of rare genetic syndromes.;
Origin ID : 568986992;
Currated CISMeF NLP mapping
Sclerodactyly is a morphological term used to describe thickening and sclerosis of
the skin and soft tissues of the fingers with resultant limitation of movement and
joint contractures. In severe cases ulceration may occur. It is typically seen in
autoimmune disorders including limited systemic sclerosis (CRST syndrome), diffuse
systemic sclerosis and mixed connective tissue disease, in which case it is likely
to be associated with Raynaud phenomenon. It may also be associated, however, with
long-standing diabetes (diabetic cheiroarthropathy), exposure to certain drugs and
or chemicals, in hand-arm vibration syndrome and in a number of rare genetic syndromes.
