Preferred Label : Oxycephaly;
ICD-11 definition : Isolated oxycephaly is a late-appearing form of nonsyndromic craniosynostosis characterized
by premature fusion of both the coronal and sagittal sutures, and, in some cases,
of the lambdoid sutures. Compensatory growth in the region of the anterior fontanel
results in a pointed or cone-shaped skull.;
ICD-11 synonym : steeple head; tower skull; egg-shaped skull; Acrocephaly; tower head; Hypsicephaly; Pyrgocephaly; Turricephaly; high-head syndrome;
ICD-11 inclusion : Turricephaly; Acrocephaly;
Origin ID : 563412852;
Automatic exact mappings (from CISMeF team)
Isolated oxycephaly is a late-appearing form of nonsyndromic craniosynostosis characterized
by premature fusion of both the coronal and sagittal sutures, and, in some cases,
of the lambdoid sutures. Compensatory growth in the region of the anterior fontanel
results in a pointed or cone-shaped skull.
