Preferred Label : Crouzon syndrome - acanthosis nigricans;
ICD-11 definition : Crouzon syndrome - acanthosis nigricans is the association of Crouzon syndrome, occuring
in 5% of cases, with acanthosis nigricans. Chiari malformation, hydrocephalus, and
atresia or stenosis of the choanas may suggest the diagnosis of Crouzon syndrome with
AN even before acanthosis appears.;
Origin ID : 549448576;
Automatic exact mappings (from CISMeF team)
Crouzon syndrome - acanthosis nigricans is the association of Crouzon syndrome, occuring
in 5% of cases, with acanthosis nigricans. Chiari malformation, hydrocephalus, and
atresia or stenosis of the choanas may suggest the diagnosis of Crouzon syndrome with
AN even before acanthosis appears.
