Preferred Label : Syringocystadenoma papilliferum;
ICD-11 definition : Syringocystadenoma papilliferum is a skin hamartoma, which is believed to derived
from apocrine sweat glands or, less often, from eccrine sweat glands. Three clinical
types have been described. The plaque type presents mostly as a hairless area in the
scalp, often in association with a sebaceous nevus of Jadassohn; the linear type,
which is usually seen on the neck or face, and the solitary nodular type, which shows
predilection for the trunk.;
ICD-11 inclusion : papillary syringocystadenoma of unspecified site;
Origin ID : 530424877;
Automatic exact mappings (from CISMeF team)
Syringocystadenoma papilliferum is a skin hamartoma, which is believed to derived
from apocrine sweat glands or, less often, from eccrine sweat glands. Three clinical
types have been described. The plaque type presents mostly as a hairless area in the
scalp, often in association with a sebaceous nevus of Jadassohn; the linear type,
which is usually seen on the neck or face, and the solitary nodular type, which shows
predilection for the trunk.
