" /> Obesity due to pro-opiomelanocortin deficiency - CISMeF





Preferred Label : Obesity due to pro-opiomelanocortin deficiency;

ICD-11 definition : Pro-opiomelanocortin (POMC) deficiency is a form of monogenic obesity resulting in severe early-onset obesity, adrenal insufficiency, red hair and pale skin.;

ICD-11 synonym : POMC deficiency; POMC - [ pro-opiomelanocortin] deficiency;

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Pro-opiomelanocortin (POMC) deficiency is a form of monogenic obesity resulting in severe early-onset obesity, adrenal insufficiency, red hair and pale skin.

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28/07/2025


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