Preferred Label : Hereditary angioedema type III;
ICD-11 definition : Hereditary angioedema due not to abnormalities of C1 inhibitor production or function
but to increased kininogenase activity and consequent increased bradykinin release.
It may be triggered by pregnancy or oestrogen-containing oral contraceptive preparations.;
ICD-11 synonym : Hereditary angioedema with FXII mutation; HAE-III - [Hereditary angioedema type III]; Inherited oestrogen-dependent angioneurotic oedema; Hereditary angioneurotic oedema type 3; Inherited oestrogen-dependent angioedema;
ICD-11 acronym : HAE-III;
Origin ID : 511982427;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
Hereditary angioedema due not to abnormalities of C1 inhibitor production or function
but to increased kininogenase activity and consequent increased bradykinin release.
It may be triggered by pregnancy or oestrogen-containing oral contraceptive preparations.
