Preferred Label : Atypical progressive supranuclear palsy;
ICD-11 definition : Atypical progressive supranuclear palsy (atypical PSP) is a group of clinical syndromes
associated with underlying PSP-tau pathology, that do not conform to the classic presentation
of PSP (Richardson syndrome), a rare late-onset neurodegenerative disease. The group
comprises PSP-Parkinsonism (PSP-P), PSP-Pure akinesia with gait freezing (PSP-PAGF),
PSP-corticobasal syndrome (PSP-CBS) and PSP-progressive non fluent aphasia (PSP-PNFA)
.;
Origin ID : 471240985;
Currated CISMeF NLP mapping
Atypical progressive supranuclear palsy (atypical PSP) is a group of clinical syndromes
associated with underlying PSP-tau pathology, that do not conform to the classic presentation
of PSP (Richardson syndrome), a rare late-onset neurodegenerative disease. The group
comprises PSP-Parkinsonism (PSP-P), PSP-Pure akinesia with gait freezing (PSP-PAGF),
PSP-corticobasal syndrome (PSP-CBS) and PSP-progressive non fluent aphasia (PSP-PNFA)
.
