Preferred Label : Aortoventricular tunnel;
ICD-11 definition : A congenital cardiovascular malformation in which there is a paravalvar communication
between the aorta and a ventricle. The aortico-left ventricular tunnel is an abnormal
paravalvar (alongside or in the vicinity of a valve) communication between the aorta
and left ventricle, commonly divided into 4 types: type I, a simple tunnel with a
slit-like opening at the aortic end and no aortic valve distortion; type II, a large
extracardiovascular aortic wall aneurysm of the tunnel with an oval opening at the
aortic end, with or without ventricular distortion; type III, intracardiovascular
aneurysm of the septal portion of the tunnel, with or without right ventricular outflow
obstruction; and type IV, a combination of types II and III. Further differentiation
within these types may be notation of right coronary artery arising from the wall
of the tunnel. If the tunnel communicates with the right ventricle, many feel that
the defect is really a ruptured sinus of Valsalva aneurysm.;
ICD-11 synonym : ventriculo-aortic tunnel; aortico-ventricular tunnel;
Origin ID : 470594532;
Automatic exact mappings (from CISMeF team)
A congenital cardiovascular malformation in which there is a paravalvar communication
between the aorta and a ventricle. The aortico-left ventricular tunnel is an abnormal
paravalvar (alongside or in the vicinity of a valve) communication between the aorta
and left ventricle, commonly divided into 4 types: type I, a simple tunnel with a
slit-like opening at the aortic end and no aortic valve distortion; type II, a large
extracardiovascular aortic wall aneurysm of the tunnel with an oval opening at the
aortic end, with or without ventricular distortion; type III, intracardiovascular
aneurysm of the septal portion of the tunnel, with or without right ventricular outflow
obstruction; and type IV, a combination of types II and III. Further differentiation
within these types may be notation of right coronary artery arising from the wall
of the tunnel. If the tunnel communicates with the right ventricle, many feel that
the defect is really a ruptured sinus of Valsalva aneurysm.
