Preferred Label : Pemphigus erythematosus;
ICD-11 definition : Pemphigus erythematosus is a rare variant of pemphigus foliaceus, and is a chronic
autoimmune skin disease with clinical and immunological features of lupus erythematosus
as well as pemphigus. It is characterized by superficial blister formation giving
scaly lesions in a butterfly distribution over the nose and cheeks as well as the
trunk and is mediated by auto-antibodies to the desmosome component desmoglein 1.;
ICD-11 synonym : Senear-Usher syndrome;
Origin ID : 399813106;
Automatic exact mappings (from CISMeF team)
Pemphigus erythematosus is a rare variant of pemphigus foliaceus, and is a chronic
autoimmune skin disease with clinical and immunological features of lupus erythematosus
as well as pemphigus. It is characterized by superficial blister formation giving
scaly lesions in a butterfly distribution over the nose and cheeks as well as the
trunk and is mediated by auto-antibodies to the desmosome component desmoglein 1.
