Preferred Label : Congenital achalasia;
ICD-11 definition : This is a congenital form of primary achalasia, an esophageal motility disorder characterized
by degeneration of the nerve cells that normally signal the brain to relax the lower
esophageal sphincter (LES).;
ICD-11 synonym : Congenital cardiospasm; Congenital oesophageal achalasia; Congenital achalasia of cardia;
ICD-11 inclusion : Congenital cardiospasm with megaloesophagus; Congenital cardiospasm with megaoesophagus; Congenital cardiospasm;
Origin ID : 398153442;
Automatic exact mappings (from CISMeF team)
This is a congenital form of primary achalasia, an esophageal motility disorder characterized
by degeneration of the nerve cells that normally signal the brain to relax the lower
esophageal sphincter (LES).