Preferred Label : Scleromyxoedema;
ICD-11 definition : Scleromyxoedema is a rare sclerotic variant of lichen myxoedematosus characterized
by a generalized papular eruption associated with dermal mucin deposition, dermal
fibroblast proliferation, diffuse dermal fibrosis and monoclonal gammopathy.;
ICD-11 synonym : Arndt-Gottron syndrome; Atypical lichen myxoedematosus; generalised papular and sclerodermoid lichen myxoedematosus;
Origin ID : 286724475;
Automatic exact mappings (from CISMeF team)
Scleromyxoedema is a rare sclerotic variant of lichen myxoedematosus characterized
by a generalized papular eruption associated with dermal mucin deposition, dermal
fibroblast proliferation, diffuse dermal fibrosis and monoclonal gammopathy.
