" /> OL-EDA-ID syndrome - CISMeF





Preferred Label : OL-EDA-ID syndrome;

ICD-11 definition : Anhidrotic ectodermal dysplasia - immunodeficiency - osteopetrosis - lymphedema syndrome is characterized by severe immunodeficiency, osteopetrosis, lymphedema and anhidrotic ectodermal dysplasia.;

ICD-11 synonym : OLEDAID - [Anhidrotic ectodermal dysplasia - immunodeficiency - osteopetrosis - lymphoedema] syndrome; OLEDAID syndrome; Anhidrotic ectodermal dysplasia - immunodeficiency - osteopetrosis - lymphoedema;

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Anhidrotic ectodermal dysplasia - immunodeficiency - osteopetrosis - lymphedema syndrome is characterized by severe immunodeficiency, osteopetrosis, lymphedema and anhidrotic ectodermal dysplasia.

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29/07/2025


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