Preferred Label : Idiopathic follicular mucinosis;
ICD-11 definition : Follicular mucinosis is a cutaneous reaction pattern characterized clinically by infiltrated
plaques with prominent hair follicles, from which mucin can sometimes be expressed,
and loss of hair; and histologically by the accumulation of acid glycosaminoglycans
in the sebaceous gland and the outer root sheath of the follicle. The clinical appearances
are varied with few or many papules or plaques confined to a localized area or widely
distributed. The causes are poorly understood but a proportion of cases are associated
with cutaneous T-cell lymphoma and this possibility must be excluded before a diagnosis
of idiopathic follicular mucinosis can be made.;
ICD-11 synonym : Alopecia mucinosa;
Origin ID : 240681277;
Automatic exact mappings (from CISMeF team)
Follicular mucinosis is a cutaneous reaction pattern characterized clinically by infiltrated
plaques with prominent hair follicles, from which mucin can sometimes be expressed,
and loss of hair; and histologically by the accumulation of acid glycosaminoglycans
in the sebaceous gland and the outer root sheath of the follicle. The clinical appearances
are varied with few or many papules or plaques confined to a localized area or widely
distributed. The causes are poorly understood but a proportion of cases are associated
with cutaneous T-cell lymphoma and this possibility must be excluded before a diagnosis
of idiopathic follicular mucinosis can be made.
