Preferred Label : Somatostatinoma;
ICD-11 definition : A rare, usually malignant neuroendocrine tumor arizing from delta cells. This neoplasm
produces large amounts of somatostatin, which may result in a syndrome characterized
by diarrhea, steatorrhea, weight loss, and gastric hyposecretion. Sixty percent are
found in the pancreas and 40% in the duodenum or jejunum. The peak incidence occurs
between 40 and 60 years of age; women are affected more than men by 2:1.;
ICD-11 synonym : Pancreatic hypersecretion of somatostatin;
Origin ID : 219879696;
Automatic exact mappings (from CISMeF team)
A rare, usually malignant neuroendocrine tumor arizing from delta cells. This neoplasm
produces large amounts of somatostatin, which may result in a syndrome characterized
by diarrhea, steatorrhea, weight loss, and gastric hyposecretion. Sixty percent are
found in the pancreas and 40% in the duodenum or jejunum. The peak incidence occurs
between 40 and 60 years of age; women are affected more than men by 2:1.
